Isolated left ventricular non-compaction: clinical characterisation of a teenage male

Authors

  • Javeria Khan Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan https://orcid.org/0000-0002-6629-6241
  • Hina Sohail Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan
  • Parveen Akhtar Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan
  • Abdul Qadir Memon Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan
  • Bisma Jalil Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan

DOI:

https://doi.org/10.47391/JPMA.10034%20

Keywords:

Left ventricular non-compaction, Isolated non-compaction of left ventricular myocardium, Left ventricular dysfunction

Abstract

Isolated Left Ventricular Non-compaction (LVNC) is a type of cardiomyopathy that usually has a genetic origin. Its diagnosis is based on findings such as deep intertrabecular recesses or sinusoids and ventricular trabeculations communicating with the left ventricular cavity. LVNC was first clinically recognised almost four decades back, yet its diagnostic and management challenges persist. In this report, we present the case of an 18-year-old boy, who presented at the National Institute of Cardiovascular Diseases, Karachi, in March 2023, with complaints of dizziness, pedal oedema, and shortness of breath. Echocardiography revealed signs suggestive of LVNC, which were confirmed conclusively on Cardiovascular Magnetic Resonance (CMR) (NC/C ratio>2.4). The patient underwent implantable cardioverter defibrillator (ICD) placement, was discharged after a smooth post-procedure recovery, and is doing well on follow-ups.

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Author Biographies

Javeria Khan, Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan

House Physician, Department of Adult Cardiology

Hina Sohail, Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan

Senior Registrar, Department of Adult Cardiology

Parveen Akhtar, Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan

Consultant Cardiologist, Department of Adult Cardiology

Abdul Qadir Memon, Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan

Resident Trainee, Department of Adult Cardiology

Bisma Jalil, Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan

Resident Trainee, Department of Adult Cardiology

Published

2024-05-24

How to Cite

Javeria Khan, Hina Sohail, Parveen Akhtar, Abdul Qadir Memon, & Bisma Jalil. (2024). Isolated left ventricular non-compaction: clinical characterisation of a teenage male. Journal of the Pakistan Medical Association, 74(6), 1183–1186. https://doi.org/10.47391/JPMA.10034

Issue

Section

Case Report